Overview
Introduction
Cystic fibrosis (CF) is the most common fatal genetic disease of young Canadians.
REx-PN
REx-PN
Cystic fibrosis (CF) is the most common fatal genetic disease of young Canadians. It thickens secretions in the lungs, pancreas, liver, intestines and reproductive tract and makes sweat unusually salty. Most provinces and territories now screen newborns for CF, and specialized CF clinics coordinate care. Most people with CF live at home and manage a demanding daily routine; many now reach middle age and beyond. RPNs meet clients with CF in paediatric and adult units, CF clinics, schools, home and community care. The RPN's role is to support daily treatments safely, administer medications correctly, perform focused assessments, recognize when the client is no longer stable and escalate promptly to the RN or primary care provider.
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